Amino Acid-Modified Infant Formula With Iron
  • Nutrition support of infants and toddlers with maple syrup urine disease (MSUD).
  • Isoleucine-, leucine- and valine-free.
  • Use under medical supervision.

  • Branched-chain amino acid-free to allow greater intake of intact protein.
  • L-carnitine (100 mg/100 g) and taurine (40 mg/100 g) to help supply amounts normally found in human milk and foods of animal origin.
  • Approximately 40% of energy as fat to help achieve acceptable formula osmolality.
  • 6.6% of energy as linoleic acid.
  • Nutrient profile specifically designed for infants and toddlers.
  • When fed according to the Abbott Nutrition Support Protocols, provides adequate amounts of all nutrients.
  • Halal.
  • Lactose-free.
  • Gluten-free.
To meet the nutrient needs of the infant or child, infant formula, breast milk or additional food choices must be given to supply protein, isoleucine, leucine and valine requirements. These may be added to the Ketonex-1 mixture or prepared separately as instructed. Depending on the specific needs of each patient, preparation will vary as prescribed by physician.


  • Give only to infants and toddlers with proven maple syrup urine disease who are under medical supervision. Must be supplemented with protein and fluid in prescribed amounts to completely meet isoleucine, leucine, valine and water requirements.
  • Not intended as a sole source of nutrition.
  • Not for IV use.
  • Do not boil mixture or use terminal sterilization.
  • Never use a microwave oven to warm formula. Serious burns can result.
  • Powdered infant formulas are not sterile and should not be fed to premature infants or infants who might have immune problems unless directed and supervised by your baby's doctor.
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List Number Item
51112 Ketonex-1 Powder / 14.1-oz (400-g) can / 6 ct


Unflavored Powder

  • Ketonex-1 Powder / 14.1-oz (400-g) can / 6 ct

Serving Size: 100 Cal

Amount Per Serving % DV % RDI
Nutrient Data
Protein Equivalent, g: 3.1    
Fat, g: 4.5    
Carbohydrate, g: 11.0    
Linoleic Acid, mg: 729    
Linolenic Acid, mg: 73    
L-Carnitine, mg: 21    
Calories: 100    
Potential Renal Solute Load, mOsm: 27.8    
Vitamin A, IU: 292    
Vitamin A, mcg RE: 87.5    
Vitamin D, IU: 63    
Vitamin D, mcg: 1.6    
Vitamin E, IU: 3    
Vitamin E, mg alpha-TE: 2.1    
Vitamin K, mcg: 10.4    
Thiamin (Vitamin B1), mcg: 396    
Riboflavin (Vitamin B2), mcg: 188    
Vitamin B6, mcg: 156    
Vitamin B12, mcg: 1.0    
Niacin, mcg: 2083    
Niacin, mg NE: 2.7    
Folic Acid (Folacin), mcg: 48    
Pantothenic Acid, mcg: 1438    
Biotin, mcg: 13.5    
Vitamin C, mg: 10.4    
Choline, mg: 16.7    
Inositol, mg: 8.3    
Calcium, mg: 120    
Calcium, mEq: 6.0    
Phosphorus, mg: 83    
Magnesium, mg: 10    
Iron, mg: 1.9    
Zinc, mg: 1.7    
Manganese, mcg: 104    
Copper, mcg: 229    
Iodine, mcg: 13.5    
Selenium, mcg: 4.2    
Chromium, mcg: 2.3    
Molybdenum, mcg: 2.5    
Sodium, mg: 39.6    
Sodium, mEq: 1.7    
Potassium, mg: 140.6    
Potassium, mEq: 3.6    
Chloride, mg: 67.7    
Chloride, mEq: 1.9    
* Prepared at 20 Cal/fl oz.

Serving Size: 100 g powder

Amount Per Serving % DV % RDI
Nutrient Data
Protein Equivalent, g: 15.0    
Fat, g: 21.7    
Carbohydrate, g: 53.0    
Linoleic Acid, mg: 3500    
Linolenic Acid, mg: 350    
L-Carnitine, mg: 100    
Calories: 480    
Potential Renal Solute Load, mOsm: 133    
Vitamin A, IU: 1400    
Vitamin A, mcg RE: 420    
Vitamin D, IU: 300    
Vitamin D, mcg: 7.5    
Vitamin E, IU: 15    
Vitamin E, mg alpha-TE: 10.1    
Vitamin K, mcg: 50    
Thiamin (Vitamin B1), mcg: 1900    
Riboflavin (Vitamin B2), mcg: 900    
Vitamin B6, mcg: 750    
Vitamin B12, mcg: 4.9    
Niacin, mcg: 10000    
Niacin, mg NE: 12.8    
Folic Acid (Folacin), mcg: 230    
Pantothenic Acid, mcg: 6900    
Biotin, mcg: 65    
Vitamin C, mg: 50    
Choline, mg: 80    
Inositol, mg: 40    
Calcium, mg: 575    
Calcium, mEq: 28.8    
Phosphorus, mg: 400    
Magnesium, mg: 50    
Iron, mg: 9    
Zinc, mg: 8    
Manganese, mcg: 500    
Copper, mcg: 1100    
Iodine, mcg: 65    
Selenium, mcg: 20    
Chromium, mcg: 11    
Molybdenum, mcg: 12    
Sodium, mg: 190    
Sodium, mEq: 8.3    
Potassium, mg: 675    
Potassium, mEq: 17.3    
Chloride, mg: 325    
Chloride, mEq: 9.2    
* Prepared at 20 Cal/fl oz.

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Unflavored Powder

  • Ketonex-1 Powder / 14.1-oz (400-g) can / 6 ct

Corn Syrup Solids, High Oleic Safflower Oil, Coconut Oil, Soy Oil, L-Alanine, L-Proline. Less than 2% of the Following: L-Lysine Acetate, L-Arginine, Calcium Phosphate, DATEM, L-Glutamine, Potassium Phosphate, Glycine, L-Tyrosine, L-Phenylalanine, L-Serine, L-Asparagine, L-Threonine, Sodium Citrate, Potassium Citrate, Magnesium Chloride, L-Histidine, L-Methionine, Calcium Carbonate, L-Glutamic Acid, Ascorbic Acid, L-Cystine Dihydrochloride, L-Tryptophan, L-Aspartic Acid, Choline Chloride, L-Carnitine, Taurine, m-Inositol, Ferrous Sulfate, Zinc Sulfate, Ascorbyl Palmitate, dl-Alpha-Tocopheryl Acetate, Niacinamide, Mixed Tocopherols, Calcium Pantothenate, Salt, Cupric Sulfate, Thiamine Chloride Hydrochloride, Manganese Sulfate, Vitamin A Palmitate, Riboflavin, Pyridoxine Hydrochloride, Folic Acid, Beta-Carotene, Potassium Iodide, Biotin, Phylloquinone, Sodium Selenate, Chromium Chloride, Sodium Molybdate, Vitamin D3, and Cyanocobalamin.

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  • Directions for Preparation and Use: Use Only As Directed by a Physician

    Your baby's health depends on carefully following these easy directions. Proper hygiene, handling and storage are important when preparing infant formula. Failure to follow these directions could result in severe harm. Ask your baby's doctor if you need to use cooled, boiled water for mixing and if you need to boil (sterilize) bottles, nipples and rings before use.
    • Wash your hands, surfaces and utensils.
    • Pour prescribed amount of water into a clean container.
    • Add prescribed amount of Ketonex-1 powder (and other ingredients if recommended).
    • Shake well for 10-15 seconds; if using a blender, mix no more than 5 seconds.
    • Pour mixture into clean feeding bottles or container; cap.
    • Once feeding begins, use within 1 hour or discard.

  • Approximate Weights for Unpacked, Level U.S. Standard Dry Household Measures for Powder*

    Household Measure (US)Weight (g)
    1 Tbsp8
    1/4 Cup30
    1/3 Cup40
    1/2 Cup60
    1 Cup120

    * For most accurate results, Ketonex-1 should be weighed on a scale that reads in grams.

Storage & Handling

  • Powder
    • Once mixed, store bottles or container in refrigerator and feed to baby or child within 24 hours
    • Store unopened or opened can at room temperature; avoid extreme temperatures.
    • Use opened can contents within 1 month.

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